The prevalence of bronchiectasis in patients with alpha-1 antitrypsin deficiency: initial report of EARCO.
Stockley, Robert A Pye, Anita De Soyza, Joshua Turner, Alice M Miravitlles, Marc
Stockley, Robert A
Pye, Anita
De Soyza, Joshua
Turner, Alice M
Miravitlles, Marc
Abstract
Background: Although bronchiectasis has been recognised as a feature of some patients with Alpha1-Antitrypsin deficiency the prevalence and characteristics are not widely known. We wished to determine the prevalence of bronchiectasis and patient characteristics. The first cohort of patients recruited to the EARCO (European Alpha1 Research Collaboration) International Registry data base by the end of 2021 was analysed for radiological evidence of both emphysema and bronchiectasis as well as baseline demographic features.
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Date
2023-08-12
Type
Article
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Orphanet J Rare Dis . 2023 Aug 12;18(1):243